2000, Cilt 13, Sayı 4, Sayfa(lar) 223-225
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COR TRIATRIATUM ASSOCIATED WITH EBSTEIN MALFORMATION OF ATRETIC MITRAL VALVE AND DOUBLE OUTLET RIGHT VENTRICLE
Funda Öztunç1, Figen Akalın2, Resmiye Beşikçi3
1Institute of Cardiology, Istanbul University, Istanbul, Turkey
2Sub-department of Pediatric Cardiology, Department of Pediatrics, School of Medicine, Marmara University, Istanbul, Turkey
3Clinic of Pediatric Cardiology, Bakırköy Maternity Hospital, Istanbul, Turkey
Keywords: Cor triatriatum, Ebstein anomaly, Mitral valve atresia, Double outlet right ventricle
Abstract
Cor triatriatum is a rare congenital cardiac anomaly and association of this pathology with Ebstein's malformation of atretic mitral valve and double outlet right ventricle has not been previously reported. We present an 11-day-old infant with this unique anomaly diagnosed by echocardiographic examination. The infant died before surgical intervention.
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